Extrarenal malignant rhabdoid tumors: radiologic findings with histopathologic correlation

نویسندگان

  • Asif Abdullah
  • Yogesh Patel
  • Terrence J. Lewis
  • Haitham Elsamaloty
  • Stephen Strobel
چکیده

Extrarenal malignant rhabdoid tumors (MRT) are extremely rare. There have been only a few cases of MRT described in the literature and even fewer in the radiology literature. We present rare uterine and hepatic MRT and their computed tomography, magnetic resonance, and ultrasound imaging features with histopathologic correlation. Although the final diagnosis is based largely on histopathology, radiologists should include MRT in their differential considerations, regardless of tumor location, when they are dealing with an extremely aggressive tumor of early childhood.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Malignant rhabdoid tumor of the liver: Findings at US, CT, and MRI, with histopathologic correlation.

Malignant rhabdoid tumors are aggressive malignancies that can rarely present as hepatic masses in the pediatric population. The imaging findings are often nonspecific and usually suggest other more common hepatic tumors. We report the radiologic appearance of malignant rhabdoid tumor in a 3-month-old female with pathologic correlation.

متن کامل

AN UNUSUAL PRESENTATION OF EXTRARENAL MALIGNANT RHABDOID TUMOR OF SOFT TISSUE: A CASE REPORT AND REVIEW OF THE LITERATURE

Extra renal extra cranial malignant rhobdoid tumors (MRT) are rare, frequently lethal and affect mostly children. No definite treatment has been made and the role of radiation therapy is poorly defined. This report explains a 14 year old girl with MRT in her neck soft tissue. She is alive with no evidence of disease 18 months after diagnosis. Through the experience with this case, we suggested...

متن کامل

Malignant Extrarenal Rhabdoid Tumor (MERT) of the Colon

Deepti Dhavaleshwar, MD; Kofi Clarke, MD, FRCP, Allegheny Health Network, Allegheny General Hospital, Division of Gastroenterology, Pittsburgh, PA Ten cases of primary colonic malignant extrarenal rhabdoid tumors (MERT) have been reported. We report a case in a 31-year-old female who presented with abdominal pain, nausea and vomiting. Her initial evaluation was significant for leukocytosis and ...

متن کامل

Malignant extrarenal rhabdoid tumor of the vulva in an adult.

Sarcomas of the vulva account for only 1-3% of all vulvar malignancies. Most common vulvar sarcomas are leiomyosarcomas, malignant fibrohistiocytomas, and aggressive angiomyxomas. Malignant rhabdoid tumor (MRT) of the kidney is a distinctive clinicopathological entity that is recognized as a highly aggressive renal tumor of childhood. Extrarenal malignant rhabdoid tumors have been proposed to e...

متن کامل

Germ-line and acquired mutations of INI1 in atypical teratoid and rhabdoid tumors.

We examined 18 atypical teratoid and rhabdoid tumors of the brain and 7 renal and 4 extrarenal rhabdoid tumors for mutations in the candidate rhabdoid tumor suppressor gene, INI1. Fifteen tumors had homozygous deletions of one or more exons of the INI1 gene, and the other 14 tumors demonstrated mutations. Germ-line mutations of INI1 were identified in four children, one with an atypical teratoi...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره 10  شماره 

صفحات  -

تاریخ انتشار 2010